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A case of Schöpf-Schulz-Passarge syndrome.
Clin Exp Dermatol. 2005 Sep; 30(5):528-30.CE

Abstract

Schöpf-Schulz-Passarge syndrome (SSPS) is a rare ectodermal dysplasia characterized by hypodontia, hypotrichosis, nail dystrophy, palmoplantar keratoderma, and periocular and eyelid margin apocrine hidrocystomas. Several other skin tumours have been described in association with this syndrome, in particular, multiple palmoplantar eccrine syringofibroadenoma (ESFA). We report a case of SSPS with diffuse palmoplantar hyperkeratosis, which was shown by histology and immunocytochemistry to be due to ESFA.

Authors+Show Affiliations

Hampton PJ
Pathology, Royal Victoria Infirmary, Queen Victoria Road, Newcastle upon Tyne, UK. hamptonpj@doctors.org.uk
Angus B
No affiliation info available
Carmichael AJ
No affiliation info available

MeSH

AgedCystsEctodermal DysplasiaEyelid DiseasesHidrocystomaHumansHypotrichosisKeratoderma, PalmoplantarMaleNail DiseasesSweat Gland NeoplasmsSyndrome

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

16045686

Citation

Hampton, P J., et al. "A Case of Schöpf-Schulz-Passarge Syndrome." Clinical and Experimental Dermatology, vol. 30, no. 5, 2005, pp. 528-30.
Hampton PJ, Angus B, Carmichael AJ. A case of Schöpf-Schulz-Passarge syndrome. Clin Exp Dermatol. 2005;30(5):528-30.
Hampton, P. J., Angus, B., & Carmichael, A. J. (2005). A case of Schöpf-Schulz-Passarge syndrome. Clinical and Experimental Dermatology, 30(5), 528-30.
Hampton PJ, Angus B, Carmichael AJ. A Case of Schöpf-Schulz-Passarge Syndrome. Clin Exp Dermatol. 2005;30(5):528-30. PubMed PMID: 16045686.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - A case of Schöpf-Schulz-Passarge syndrome. AU - Hampton,P J, AU - Angus,B, AU - Carmichael,A J, PY - 2005/7/28/pubmed PY - 2005/12/13/medline PY - 2005/7/28/entrez SP - 528 EP - 30 JF - Clinical and experimental dermatology JO - Clin Exp Dermatol VL - 30 IS - 5 N2 - Schöpf-Schulz-Passarge syndrome (SSPS) is a rare ectodermal dysplasia characterized by hypodontia, hypotrichosis, nail dystrophy, palmoplantar keratoderma, and periocular and eyelid margin apocrine hidrocystomas. Several other skin tumours have been described in association with this syndrome, in particular, multiple palmoplantar eccrine syringofibroadenoma (ESFA). We report a case of SSPS with diffuse palmoplantar hyperkeratosis, which was shown by histology and immunocytochemistry to be due to ESFA. SN - 0307-6938 UR - https://wwww.unboundmedicine.com/medline/citation/16045686/A_case_of_Schöpf_Schulz_Passarge_syndrome_ DB - PRIME DP - Unbound Medicine ER -