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Ectodermal dysplasias associated with clefting: significance of scalp dermatitis.
J Am Acad Dermatol. 1992 Aug; 27(2 Pt 1):249-56.JA

Abstract

Several clinical syndromes are characterized by ectodermal dysplasia (ED) in association with clefting of the lip and/or palate. The three most commonly recognized entities are (1) the EEC syndrome (ectodermal dysplasia, ectrodactyly, cleft lip/palate); (2) the Rapp-Hodgkin syndrome with ectodermal dysplasia, cleft lip/palate, and mid facial hypoplasia; and (3) the Hay-Wells or AEC syndrome (ankyloblepharon, ectodermal defects, cleft lip/palate). The clinical characteristics of these entities as well as several less common syndromes are reviewed and summarized. The presence of scalp dermatitis in patients with the AEC syndrome and less often the Rapp-Hodgkin syndrome is emphasized.

Authors+Show Affiliations

Department of Dermatology, Yale University School of Medicine, New Haven, CT 06510.No affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article
Review

Language

eng

PubMed ID

1341424

Citation

Fosko, S W., et al. "Ectodermal Dysplasias Associated With Clefting: Significance of Scalp Dermatitis." Journal of the American Academy of Dermatology, vol. 27, no. 2 Pt 1, 1992, pp. 249-56.
Fosko SW, Stenn KS, Bolognia JL. Ectodermal dysplasias associated with clefting: significance of scalp dermatitis. J Am Acad Dermatol. 1992;27(2 Pt 1):249-56.
Fosko, S. W., Stenn, K. S., & Bolognia, J. L. (1992). Ectodermal dysplasias associated with clefting: significance of scalp dermatitis. Journal of the American Academy of Dermatology, 27(2 Pt 1), 249-56.
Fosko SW, Stenn KS, Bolognia JL. Ectodermal Dysplasias Associated With Clefting: Significance of Scalp Dermatitis. J Am Acad Dermatol. 1992;27(2 Pt 1):249-56. PubMed PMID: 1341424.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Ectodermal dysplasias associated with clefting: significance of scalp dermatitis. AU - Fosko,S W, AU - Stenn,K S, AU - Bolognia,J L, PY - 1992/8/1/pubmed PY - 1992/8/1/medline PY - 1992/8/1/entrez SP - 249 EP - 56 JF - Journal of the American Academy of Dermatology JO - J Am Acad Dermatol VL - 27 IS - 2 Pt 1 N2 - Several clinical syndromes are characterized by ectodermal dysplasia (ED) in association with clefting of the lip and/or palate. The three most commonly recognized entities are (1) the EEC syndrome (ectodermal dysplasia, ectrodactyly, cleft lip/palate); (2) the Rapp-Hodgkin syndrome with ectodermal dysplasia, cleft lip/palate, and mid facial hypoplasia; and (3) the Hay-Wells or AEC syndrome (ankyloblepharon, ectodermal defects, cleft lip/palate). The clinical characteristics of these entities as well as several less common syndromes are reviewed and summarized. The presence of scalp dermatitis in patients with the AEC syndrome and less often the Rapp-Hodgkin syndrome is emphasized. SN - 0190-9622 UR - https://wwww.unboundmedicine.com/medline/citation/1341424/Ectodermal_dysplasias_associated_with_clefting:_significance_of_scalp_dermatitis_ L2 - https://linkinghub.elsevier.com/retrieve/pii/0190-9622(92)70179-J DB - PRIME DP - Unbound Medicine ER -